1Contraindications for succinylcholine in _____ patients d/t causing _________; family history of ______, & _______
- Duchenne muscular dystrophy
- Rhabdomyolysis, life threatening hyperkalemia, brady arrhythmia & inc. ICP
- malignant hyperthermia.
- Crush injuries
2For a child who is hospitalized, what is the MOST significant predisposing factor for pulmonary embolism?
central venous catheter
3Injuries MOST frequently occurring with abusive head trauma include retinal hemorrhages and:
rib fractures and classic metaphyseal lesions
4The combination of _____, _____, & _____ should raise red flags for leukemia
hyperleukocytosis (inc WBC), thrombocytopenia (dec plt), and anemia
5When providing education to parents of a toddler newly diagnosed with Rett syndrome, appropriate guidance includes to expect
an increase in autistic type behaviors as the child ages.
6An adolescent with bulimia nervosa who discloses vomiting and laxative use is at risk for which metabolic abnormalities?
hypochloremia, hypokalemia, metabolic alkalosis
7A 2 year old with previously undiagnosed, uncomplicated coarctation of the aorta has normal growth and development. The stenosis is located just distal to the left subclavian artery. Medical management includes
monitoring upper extremity blood pressures for hypertension.
8An adolescent with lymphoma develops gross hematuria. Physical examination reveals new-onset hypertension, and urinalysis is significant for proteinuria. Which of the following diagnostic tests would BEST confirm the type of nephrotic syndrome?
complement levels
9Following spinal fusion surgery for scoliosis, an adolescent develops mid-abdominal pain and bilious emesis. Nonpharmacological therapy to alleviate symptoms includes placing in which of the following positions?
prone or knee-chest
10A 2 month old with an infantile hemangioma around the left eye is being evaluated for propranolol therapy. Which of the following findings would be considered a potential CONTRAINDICATION?
sinus bradycardia
11Following the removal of the spleen, vaccination reccommendations include _____, ______, & _____ given within ______ following the splenectomy.
- pneumococcal (PCV), H. influenzae (HiB), and meningococcal vaccines
- 14 days
12pt. w/ myasthenia gravis presents with acute, severe worsening of neuromuscular weakness and respiratory function. To ensure appropriate treatment, it is the MOST important to distinguish myasthenic crisis from
cholinergic crisis
13An infant is admitted with SVT, which is now stabilized. Which of the following medications is best prescribed FIRST for ongoing medical therapy?
propranolol
14Which of the following findings seen on echocardiogram is MOST consistent with Marfan syndrome?
mitral valve prolapse
15Marfan syndrome is a genetic disorder caused by mutations in the ______ gene. predominantly affects ______ with phenotypic features, including.......
- FBN1
- males
- tall height, hyperflexibility, arachnodactyly, scoliosis, and pectus carinatum.
16The life-threatening features of marfan syndrome include _______ & ______. The leading causes of morbidity and mortality include ______ & ______
- valvular insufficiency and aortic root dilation
- mitral valve prolapse and aortic dissection.
178 month old presents with a history of increased sleeping, poor feeding, and one stool in the last six days. Physical exam findings include a weak cry and lack of a social smile. The MOST likely diagnosis is:
infant botulism
18The main objective of parenteral nutrition for a child with septic shock who is mechanically ventilated and receiving inotropic support is to maintain:
positive nitrogen balance
192-day history of decreased oral intake, irritability, and “sleeping more than usual.” Laboratory results are remarkable for an anion gap acidosis, inc lactate, and inc. ammonia. Which of the following diagnoses is MOST likely?
inborn error of metabolism
20Within 2-3 days of initiating parenteral nutrition, which of the following laboratory assessments should be monitored to direct adjustment of the formulation?
triglycerides
21adolescent who is being admitted following pulmonary valve replacement surgery, which of the following hemodynamic findings are MOST concerning for cardiac tamponade?
CVP 20 mmHg and BP 70/55 mmHg
22The MOST common viral infection following pediatric lung transplantation is:
cytomegalovirus
23full term presents with sepsis and requires mechanical ventilation. A viral panel is positive for enterovirus and seizures are present on EEG. Epinephrine, dopamine, and vasopressin are required to maintain adequate hemodynamics. The MOST likely diagnosis is:
myocarditis
24Children with Down syndrome have a higher incidence of developing _______. Clinical findings of leukemia include .....
- leukemia
- persistent fevers, anemia, thrombocytopenia (dec plt), and either inc or dec WBC (leukopenia).
25adolescent receiving a propofol infusion develops refractory bradycardia. Which of the following additional clinical findings completes the diagnostic criteria for propofol infusion syndrome?
metabolic acidosis
26adolescent presents with acute scrotal pain of 5 hours duration, a unilateral absent cremasteric reflex, and nausea and vomiting. The FIRST step in management should be
emergent surgical referral for testicular torsion
27Enteral nutrition is initiated in a child with severe malnutrition. Laboratory values indicative of refeeding syndrome include a magnesium level of 1.5 mg/dL, and:
phosphate of 3.0 mg/dL and potassium of 2.8 mEq/L
28In a previously healthy, immunized infant who has a urinalysis positive for leukocyte esterase and nitrates, which of the following findings is MOST supportive of a diagnosis of pyelonephritis?
fever of 39.2° C (102.6° F)
29IgA vasculitis (formerly Henoch-Schönlein purpura) is an acute vasculitis that is the most common cause of purpura in children without thrombocytopenia. Abdominal pain, rash, polyarthritis, and kidney disease are the classic tetrad.
.....